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Question 1 of 20
1. Question
A 60-year-old man has a painful right knee and a slightly enlarged spleen. Hematology results include:
test
result
hemoglobin
15 g/dL (150 g/L)
absolute neutrophil count
10.0 x 103/μL (10.0 x 109/L)
platelet count
900×103/μL (900 x 109/L)
uncorrected retic count
1%
morphology
normal red cell morphology and indices a slight increase in bands rare metamyelocyte and myelocyte giant and bizarre-shaped platelets
This is most compatible with:
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Question 2 of 20
2. Question
The type of bleeding that is the most characteristic in patients with platelet disorders is:
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Question 3 of 20
3. Question
When reviewing platelet morphology on a blood smear, the presence of giant platelets is noted. This may indicate:
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Question 4 of 20
4. Question
A patient with multimer pattern that has all bands present but in decreased concentrations would be diagnosed with:
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Question 5 of 20
5. Question
Which characteristic of Bernard-Soulier syndrome helps distinguish it from von Willebrand disease?
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Question 6 of 20
6. Question
Which of the following characteristics are common between Hěrmanský-Pudlák and Chédiak-Higashi syndromes?
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Question 7 of 20
7. Question
Patients with Wiscott-Aldrich syndrome present with:
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Question 8 of 20
8. Question
When evaluating a patient for von Willebrand disorder, the ABO blood type that has the lowest level of vWF is:
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Question 9 of 20
9. Question
Which subtype of von Willebrand disease is the most common?
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Question 10 of 20
10. Question
Which of the following types of von Willebrand disease should not be treated with DDAVP?
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Question 11 of 20
11. Question
TTP presents with a pentad of symptoms that does not include:
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Question 12 of 20
12. Question
A 40-year-old female has pinpoint hemorrhages on her legs, with an Hct of 43% and a platelet count of 19 x 103/μL (19 x 109/L). Steroids fail to increase platelet count. The patient’s diagnosis is:
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Question 13 of 20
13. Question
A 60-year-old female presents with blurred vision, confusion, and petechiae with a platelet count of 29 x 103/μL (29 x 109/L).
test
result
PT
12.1 seconds (11.4-13.5 seconds)
aPTT
32.6 seconds (25-35 seconds)
The CBC RBC morphology shows schistocytes. The differential diagnosis should include:
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Question 14 of 20
14. Question
One of the main difference between TTP and HUS is:
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Question 15 of 20
15. Question
Several hours after birth an infant develops petechiae, purpuric hemorrhages and a platelet count of 21 x 103/μL (21 x 109/L). The most likely diagnosis is:
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Question 16 of 20
16. Question
In TTP, a deficiency of ADAMTS13 causes clotting because of:
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Question 17 of 20
17. Question
An orthopedic patient who is on heparin has a platelet count of 50 x 103/μL (50 x 109/L);his platelet count the previous day was 120 x 103/μL (120 x 109/L). The patient is tested for HIT and has a positive result. The first step in the treatment of HIT is:
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Question 18 of 20
18. Question
In HELLP syndrome patients present with:
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Question 19 of 20
19. Question
von Willebrand factor serves as a stabilizer for:
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Question 20 of 20
20. Question
The platelet disorder in which the abnormality is due to a defect in platelet aggregation is:
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